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KMID : 0032220090210010056
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Annals of Dermatology
2009 Volume.21 No. 1 p.56 ~ p.59
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A Case of Incontinentia Pigmenti Associated with Multiorgan Abnormalities.
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Chung Woon-Kyong
Chang Sung-Eun
Lee Mi-Woo
Choi Jee-Ho
Moon Kee-Chan
Lee Deok-Woo
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Abstract
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Incontinentia pigmenti is a systemic disorder affecting the skin, teeth, eyes, nervous tissue, hair, nails, musculoskeletal system, and heart. We describe an 11-month-old girl with incontinentia pigmenti associated with a ventricular septal defect, left hemiatrophy, hemangiomas, an abnormal labial frenum, and spastic cerebral palsy manifested as left hemiplegia and developmental delay. We believe this patient illustrates that incontinentia pigmenti is a systemic disorder necessitating a multidisciplinary approach to management.
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KEYWORD
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Genodermatosis, Incontinentia pigmenti, Systemic disorder
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